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of the North Caucasus
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ISSN 2073-8137

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Hystyocytoid cardiomyopathy in the newborn with extremely low body weight

[Notes from practice]
Ludmila Kulida; Olga Saryeva; Mariya Malysheva;

A description of the clinical observation of histiocytoid cardiomyopathy in an extremely low birth weight of a newborn girl is given. This is a genetically determined form of cardiomyopathy associated with a mutation of the gene encoding the proteins of electron mitochondrial transport. Observation reflects the main clinical manifestations and features of myocardial restructuring characteristic of this form of cardiomyopathy.


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Keywords: histiocytoid cardiomyopathy, mitochondrial myopathy, cardiac rhythm disturbance, a newborn with extremely low body weight

Stavropol State Medical Academy
Pyatigorsk State Research Institute of Balneotherapeutics
Pyatigorsk State Pharmaceutical Academy