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https://doi.org/10.14300/mnnc.2022.17023

Clinical case of pulmonary alveolar proteinosis in a child with primary immunodeficiency

[Notes from practice]
Natalia Anatolievna Ilyenkova; Olga Sergeevna Konopleva; Surenovna Zhigunova Olesya;

Pulmonary alveolar proteinosis is a rare lung disease characterized by dysfunction of alveolar macrophages and accumulation of surfactant in the alveoli. In the given clinical observation, a rare case of pulmonary alveolar proteinosis in a young child was demonstrated, confirmed by instrumental and morphological methods of research.

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References:
1. Kumar А., Abdelmalak B., Inoue Y., Culver D. A. Pulmonary alveolar proteinosis in adults: pathophysiology and clinical approach. Lancet Respir. Med. 2018;6(7):554-565. https://doi.org/10.1016/S2213-2600(18)30043-2
2. Griese M. Pulmonary alveolar proteinosis: a comprehensive clinical perspective. Pediatrics. 2017;140(2). https://doi.org/10.1542/peds.2017-0610
3. Karoli N. A., Arhangel’skaya E. E., Zarmanbetova O. T. Legochnyj al’veolyarnyj proteinoz: klinicheskij sluchaj. Arhiv vnutrennej mediciny. – Archive of internal medicine. 2020;3:237-242. (In Russ.). https://doi.org/10.20514/2226-6704-2020-10-3-237-242
4. Concepción-Urteaga L. A., Rodríguez-Hidalgo L. A., Cornejo-Portella J. L., Alquizar-Horna O. N., Aguilar-Villanueva D. A. [et al.]. Pulmonary alveolar proteinosis: a case report. Medwave. 2017;17(8):e7040. https://doi.org/10.5867/medwave.2017.08.7040

Keywords: pulmonary alveolar proteinosis, clinic, diagnosis, children